Cystic fibrosis (CF) is a genetic disorder that affects mostly the lungs, but also the pancreas, liver, kidneys, and intestine.[Long-term issues include difficulty breathing and coughing up mucus as a result of frequent lung infections.Other signs and symptoms may include sinus infections, poor growth, fatty stool, clubbing of the fingers and toes, and infertility in some males. Different people may have different degrees of symptoms.
1.Airway clearance techniques should be performed across the lifespan in CF (C)
2. The ACBT is an effective form of airway clearance and can be used by people with acute and chronic lung disease independently or in conjunction with other ACTs (B)
3. PEP therapy, oscillating PEP and autogenic drainage are effective forms of airway clearance which can be performed independently (B)
4. Postural drainage in head-down positions should not be used routinely in infants with CF (B) or in patients of any age with known or suspected GOR (C). Modified postural drainage is recommended in infants and young children where active participation in airway clearance therapy is not possible (B)
5. Physical exercise may be used to reduce mechanical impedance of sputum (B), achieve short term improvements in pulmonary function (A) and improve ease of expectoration (B)
